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Milestones in Drug Therapy

Treatment of Cystic Fibrosis and Other Rare Lung Diseases

Editors: Azuma, Arata, Schechter, Michael S. (Eds.)

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  • Offers up-to-date information on the research background and treatment of these pulmonary diseasesExplores basic molecular biological research as well as clinical applicationsPrimarily aimed at researchers and clinicians

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eBook $129.00
price for USA (gross)
  • ISBN 978-3-0348-0977-1
  • Digitally watermarked, DRM-free
  • Included format: PDF, EPUB
  • ebooks can be used on all reading devices
  • Immediate eBook download after purchase
Hardcover $169.99
price for USA
  • ISBN 978-3-0348-0975-7
  • Free shipping for individuals worldwide
  • Usually dispatched within 3 to 5 business days.
About this book

This volume describes the pathogenesis and pathophysiology of several pulmonary diseases as well as their treatment. It also discusses the underlying genetic and molecular biological basis, which opens the way for new treatments for these conditions.

It focuses on the treatment of cystic fibrosis including CFTR (cystic fibrosis transmembrane-conductance regulator) modulator therapies, drug therapies that augment airway surface liquid as well as anti-inflammatory and anti-infective therapies. Further topics include long-term, low-dose macrolide therapy for diffuse panbronchiolitis; novel agents for previously untreatable idiopathic pulmonary fibrosis; possible new treatments for pulmonary alveolar proteinosis (PAP); and multiple novel therapeutic targets for treating lymphangiomyomatosis. Research into these conditions has led to major advances in our understanding of the underlying genetic and molecular basis of this disease, and to dramatic improvements in survival and quality of life for affected individuals.



Reviews

“The purpose is to focus on recent advances in understanding the molecular basis of these diseases, and how this understanding has helped develop novel targeted therapies. … The audience is clinicians, students, and researchers who want a deeper understanding of the pathogenesis and recent advances in the therapy of these rare diseases. … It should serve as a useful addition to the personal library of any interested pulmonologist or lung disease researcher.” (Santosh Dhungana, Doody's Book Reviews, April, 2017)


                

Table of contents (13 chapters)

Table of contents (13 chapters)

Buy this book

eBook $129.00
price for USA (gross)
  • ISBN 978-3-0348-0977-1
  • Digitally watermarked, DRM-free
  • Included format: PDF, EPUB
  • ebooks can be used on all reading devices
  • Immediate eBook download after purchase
Hardcover $169.99
price for USA
  • ISBN 978-3-0348-0975-7
  • Free shipping for individuals worldwide
  • Usually dispatched within 3 to 5 business days.

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Bibliographic Information

Bibliographic Information
Book Title
Treatment of Cystic Fibrosis and Other Rare Lung Diseases
Editors
  • Arata Azuma
  • Michael S. Schechter
Series Title
Milestones in Drug Therapy
Copyright
2017
Publisher
Springer Basel
Copyright Holder
Springer International Publishing Switzerland
eBook ISBN
978-3-0348-0977-1
DOI
10.1007/978-3-0348-0977-1
Hardcover ISBN
978-3-0348-0975-7
Series ISSN
2296-6056
Edition Number
1
Number of Pages
VIII, 263
Number of Illustrations
19 b/w illustrations, 14 illustrations in colour
Topics